{"created":"2023-06-20T15:49:06.757107+00:00","id":3667,"links":{},"metadata":{"_buckets":{"deposit":"20426657-497c-4f5a-bd93-dbcad8b5add7"},"_deposit":{"created_by":4,"id":"3667","owners":[4],"pid":{"revision_id":0,"type":"depid","value":"3667"},"status":"published"},"_oai":{"id":"oai:hama-med.repo.nii.ac.jp:00003667","sets":["1:75:76"]},"author_link":["10833","10834","10835","10836","10837","10838","10839","10840"],"item_3_biblio_info_5":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2021-03-15","bibliographicIssueDateType":"Issued"},"bibliographicIssueNumber":"1","bibliographicPageEnd":"35","bibliographicPageStart":"29","bibliographicVolumeNumber":"1","bibliographic_titles":[{"bibliographic_title":"浜松医科大学小児科学雑誌","bibliographic_titleLang":"ja"},{"bibliographic_title":"Hamamatsu Journal of Pediatrics","bibliographic_titleLang":"en"}]}]},"item_3_description_9":{"attribute_name":"抄録","attribute_value_mlt":[{"subitem_description":"Susac症候群は自己免疫的機序により頭蓋内、内耳、網膜の微小血管に炎症を来し、脳症、難聴、視力障害を生じる稀な症候群である。Susac症候群の多くは20?40歳で発症する。2歳10か月と若年で発症した不全型Susac症候群の1例を経験したので報告する。2歳10か月時に失調症状が出現し、経過中に脳梁と大脳深部白質に散在する頭部MRIT2強調像高信号の病巣、左網膜血管の微小炎症を認めた。頭痛や四肢の痺れを反復し、8歳7か月時髄液蛋白上昇と頭部MRIで白質新規病変を認めた。本例では聴力低下を認めず、不全型Susac症候群と診断した。mPSLパルスとPSL内服で治療するも再燃した。シクロフォスファミドパルス、月1回の免疫グロブリン大量療法（IVIG）、ミコフェノール酸モフェチルを併用し、12か月間再燃なく経過している。Susac症候群は、診断を確実に行うとともに、約60％で後遺症を呈するため、十分な免疫抑制療法による再燃防止が必要である。","subitem_description_language":"ja","subitem_description_type":"Abstract"}]},"item_3_publisher_6":{"attribute_name":"出版者","attribute_value_mlt":[{"subitem_publisher":"浜松医科大学小児科学雑誌編集部","subitem_publisher_language":"ja"}]},"item_3_relation_27":{"attribute_name":"医中誌論文ID","attribute_value_mlt":[{"subitem_relation_type":"isIdenticalTo","subitem_relation_type_id":{"subitem_relation_type_id_text":"2021237781","subitem_relation_type_select":"ICHUSHI"}}]},"item_3_source_id_20":{"attribute_name":"EISSN","attribute_value_mlt":[{"subitem_source_identifier":"2436-2433","subitem_source_identifier_type":"EISSN"}]},"item_3_version_type_32":{"attribute_name":"著者版フラグ","attribute_value_mlt":[{"subitem_version_resource":"http://purl.org/coar/version/c_970fb48d4fbd8a85","subitem_version_type":"VoR"}]},"item_access_right":{"attribute_name":"アクセス権","attribute_value_mlt":[{"subitem_access_right":"open access","subitem_access_right_uri":"http://purl.org/coar/access_right/c_abf2"}]},"item_creator":{"attribute_name":"著者","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"伊藤, 祐介","creatorNameLang":"ja"},{"creatorName":"ITO, Yusuke","creatorNameLang":"en"}],"nameIdentifiers":[{"nameIdentifier":"10833","nameIdentifierScheme":"WEKO"}]},{"creatorNames":[{"creatorName":"石垣, 英俊","creatorNameLang":"ja"},{"creatorName":"ISHIGAKI, Hidetoshi","creatorNameLang":"en"}],"nameIdentifiers":[{"nameIdentifier":"10834","nameIdentifierScheme":"WEKO"}]},{"creatorNames":[{"creatorName":"漆畑, 伶","creatorNameLang":"ja"},{"creatorName":"URUSHIBATA, Rei","creatorNameLang":"en"}],"nameIdentifiers":[{"nameIdentifier":"10835","nameIdentifierScheme":"WEKO"}]},{"creatorNames":[{"creatorName":"平出, 拓也","creatorNameLang":"ja"},{"creatorName":"HIRAIDE, Takuya","creatorNameLang":"en"}],"nameIdentifiers":[{"nameIdentifier":"10836","nameIdentifierScheme":"WEKO"}]},{"creatorNames":[{"creatorName":"杉江, 秀夫","creatorNameLang":"ja"},{"creatorName":"SUGIE, Hideo","creatorNameLang":"en"}],"nameIdentifiers":[{"nameIdentifier":"10837","nameIdentifierScheme":"WEKO"}]},{"creatorNames":[{"creatorName":"鈴木, 寛子","creatorNameLang":"ja"},{"creatorName":"SUZUKI, Hiroko","creatorNameLang":"en"}],"nameIdentifiers":[{"nameIdentifier":"10838","nameIdentifierScheme":"WEKO"}]},{"creatorNames":[{"creatorName":"佐藤, 美保","creatorNameLang":"ja"},{"creatorName":"Sato, Miho","creatorNameLang":"en"}],"nameIdentifiers":[{"nameIdentifier":"10839","nameIdentifierScheme":"WEKO"}]},{"creatorNames":[{"creatorName":"福田, 冬季子","creatorNameLang":"ja"},{"creatorName":"FUKUDA, Tokiko","creatorNameLang":"en"}],"nameIdentifiers":[{"nameIdentifier":"10840","nameIdentifierScheme":"WEKO"}]}]},"item_files":{"attribute_name":"ファイル情報","attribute_type":"file","attribute_value_mlt":[{"accessrole":"open_date","date":[{"dateType":"Available","dateValue":"2021-03-15"}],"displaytype":"detail","filename":"hjop_1_1_29.pdf","filesize":[{"value":"563.2 kB"}],"format":"application/pdf","licensetype":"license_note","mimetype":"application/pdf","url":{"label":"hjop_1_1_29","objectType":"fulltext","url":"https://hama-med.repo.nii.ac.jp/record/3667/files/hjop_1_1_29.pdf"},"version_id":"222db68d-6a58-4a94-88df-55f3702dc2df"}]},"item_keyword":{"attribute_name":"キーワード","attribute_value_mlt":[{"subitem_subject":"Susac症候群","subitem_subject_language":"ja","subitem_subject_scheme":"Other"},{"subitem_subject":"中枢神経血管炎","subitem_subject_language":"ja","subitem_subject_scheme":"Other"},{"subitem_subject":"脳症","subitem_subject_language":"ja","subitem_subject_scheme":"Other"},{"subitem_subject":"網膜動脈分枝閉鎖症","subitem_subject_language":"ja","subitem_subject_scheme":"Other"},{"subitem_subject":"難聴","subitem_subject_language":"ja","subitem_subject_scheme":"Other"}]},"item_language":{"attribute_name":"言語","attribute_value_mlt":[{"subitem_language":"jpn"}]},"item_resource_type":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"resourcetype":"journal article","resourceuri":"http://purl.org/coar/resource_type/c_6501"}]},"item_title":"小児期発症の不全型Susac症候群の1例","item_titles":{"attribute_name":"タイトル","attribute_value_mlt":[{"subitem_title":"小児期発症の不全型Susac症候群の1例","subitem_title_language":"ja"},{"subitem_title":"A Case Report of Childhood Onset Incomplete Susac Syndrome","subitem_title_language":"en"}]},"item_type_id":"3","owner":"4","path":["76"],"pubdate":{"attribute_name":"PubDate","attribute_value":"2021-03-15"},"publish_date":"2021-03-15","publish_status":"0","recid":"3667","relation_version_is_last":true,"title":["小児期発症の不全型Susac症候群の1例"],"weko_creator_id":"4","weko_shared_id":-1},"updated":"2024-03-22T03:01:23.037770+00:00"}