| Item type |
学術雑誌論文 / Journal Article(1) |
| 公開日 |
2022-04-08 |
| タイトル |
|
|
タイトル |
手術的加療にて改善した側頭骨PMT（Phosphaturic Mesenchymal Tumor）例 |
| タイトル |
|
|
タイトル |
A Case of Temporal Bone Phosphaturic Mesenchymal Tumor That Was Treated by Surgery |
|
言語 |
en |
| 言語 |
|
|
言語 |
jpn |
| キーワード |
|
|
主題 |
temporal bone |
| キーワード |
|
|
主題 |
phosphaturic mesenchymal tumor |
| キーワード |
|
|
主題 |
tumor-induced osteomalacia |
| 資源タイプ |
|
|
資源タイプ識別子 |
http://purl.org/coar/resource_type/c_6501 |
|
資源タイプ |
journal article |
| 著者 |
大和谷, 崇
中西, 啓
遠藤, 志織
細川, 誠二
峯田, 周幸
|
| 書誌情報 |
耳鼻咽喉科臨床 補冊 = Practica oto-rhino-laryngologica. Suppl.
巻 156,
p. 21-25,
発行日 2021-02-01
|
| 出版者 |
|
|
出版者 |
耳鼻咽喉科臨床学会 |
| 出版者 |
|
|
出版者 |
The Society of Practical Otolaryngology |
| 権利 |
|
|
権利情報 |
出版者の許諾を得て掲載 |
| 抄録 |
|
|
内容記述タイプ |
Abstract |
|
内容記述 |
Phosphaturic mesenchymal tumor (PMT) is a rare neoplasm that secretes fibroblast growth factor 23 (FGF23), which suppresses re-absorption of phosphorus in the renal tubules and leads to chronic hypophosphatemia, thereby resulting in tumor-induced osteomalacia (TIO). Herein, we report a patient who had suffered multiple fractures and was diagnosed as having PMT in his left temporal bone two years later the appearance of the first symptom. For his first consultation at our department, the patient was transported to the hospital on a stretcher, as he had found it difficult to turn over in bed due to generalized bone pain and multiple pathological fractures. Examination revealed that the tumor had already spread deep into the skull base; therefore, considering the general condition of the patient, we determined that radical surgery would be difficult. Transmastoid surgical debulking was performed three months after the first consultation at our department, and the patient’s quality of life improved after the surgery. However, 10 months after the surgical debulking procedure, since we did not observe any improvements in his clinical findings, we performed radical surgery together with the neurosurgeons, which yielded good results. This case suggests that radical surgery is essential for the treatment of PMT. Even in cases where radical surgery is initially deemed to be challenging, gradual steps towards radical surgical treatment may be possible. |
| 注記 |
|
|
内容記述 |
浜松医科大学医学部耳鼻咽喉科・頭頸部外科学教室 峯田周幸教授退任記念論文集～症例から学ぶ～ |
| 注記 |
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|
内容記述 |
Festschrift for Professor Hiroyuki Mineta In Hornor of His Retirement as Chairman of Hamamatsu University School of Medicine |
| ISSN |
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収録物識別子タイプ |
ISSN |
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収録物識別子 |
0912-1870 |
| EISSN |
|
|
収録物識別子タイプ |
ISSN |
|
収録物識別子 |
2185-1557 |
| 医中誌論文ID |
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|
関連タイプ |
isIdenticalTo |
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|
識別子タイプ |
ICHUSHI |
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|
関連識別子 |
2021267585 |
| 出版社DOI |
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|
関連タイプ |
isIdenticalTo |
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|
識別子タイプ |
DOI |
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|
関連識別子 |
10.5631/jibirinsuppl.156.21 |
| 著者版フラグ |
|
|
出版タイプ |
VoR |
|
出版タイプResource |
http://purl.org/coar/version/c_970fb48d4fbd8a85 |
耳鼻臨床補冊-156-21.pdf (1.6 MB)
